Résumé

Budd-Chiari syndrome (SBC), defined by obstruction of the suprahepatic veins or the suprahepatic inferior vena cava, presents with an acute, subacute or chronic picture, but exceptionally as fulminant hepatitis. We report the case of a 24-year-old patient, without any particular pathological history, admitted in a picture of fulminant hepatitis, whose etiological assessment was in favor of SBC. The course was marked by the aggravation of his hepatic encephalopathy and death two days later by a major digestive hemorrhage. The therapeutic management of fulminant SBC is poorly codified, with a high mortality rate.

Mot-clés :

Budd-Chiari Syndrome, Suprahepatic Veins, Fulminant Hepatitis, Mortality