Résumé

Diastematomyelia is a rare congenital neural tube defect characterized by sagittal splitting of the spinal cord. This report describes the case of a 13-year-old adolescent with multiple type II diastematomyelia, diagnosed following progressive tetraparesis in the absence of typical cutaneous or vertebral stigmata. Magnetic resonance imaging (MRI) revealed spinal cord duplication across multiple thoracic segments (T1–T4/T5 and T6–T8). The atypical clinical presentation, including psychomotor delay, learning difficulties, and progressive neurological deficits, highlights the diverse manifestations of this condition. Early surgical intervention was recommended to prevent further neurological deterioration. This case underscores the importance of considering the diagnosis in the presence of unexplained neurological symptoms, even without cutaneous signs, and confirms the central role of MRI in the diagnostic workup.

Mot-clés :

Diastematomyelia, Spinal Malformation, Mri, Surgery